Multicenter Study on Late Outcomes of Biventricular Repair of Double Outlet Right Ventricle

This retrospective multicenter study examined late surgical outcomes for children from low and middle income countries with double outlet right ventricle (DORV). DORV was defined as both great arteries arising entirely or mostly from the right ventricle. A total of 81 consecutive DORV repairs were performed between 1996 and 2022. Six subtypes of DORV were divided into two overall groups: (i) DORV-committed ventricular septal defect (VSD) and (ii) DORV-noncommitted (nc) VSD. Four Fontan patients were excluded, and three patients were lost to follow up. Overall perioperative mortality was 7.4 percent. Overall, 1--year survival was 86 percent. Early mortality was similar in both groups. There was a trend toward satisfactory outcome of biventricular repair for simple DORV with committed VSD compared with complex DORV with ncVSD.