Discordant Atrioventricular Connections 4: Rarer Lesions associated with Congenitally Corrected Transposition

In this last video in the series, we examine three specimens with rarer lesions associated with congenitally corrected transposition. The first is an example of a heart with discordant atrioventricular, but concordant ventriculo-arterial connections. In this setting, the circulatory patterns are those of regular transposition, and such lesions are perfect for surgical correction using atrial redirection operations such as the Mustard or Senning procedures. The second example shows discordant atrioventricular connections with double outlet from the morphologically right ventricle. This is not strictly congenitally corrected transposition, but is a "close-cousin" of the lesions with "double discordance". The final specimen is an example of congenitally corrected transposition with mirror-imagery of the atrial chambers. Then, in keeping with the discordant atrioventricular connections, there is right hand ventricular topology, the morphologically right ventricle being right-sided in this combination. The specimen also has a ventricular septal defect and pulmonary stenosis.